Learning that you have a rare disorder of the reproductive system can turn your world upside down, especially if you are only a teenager when you receive this news. “Mayer-Rokitansky-Küster-Hauser Syndrome” or MRKH is a disorder that affects 1 in 5,000 women and can also affect other internal organs, skeletal development, and hearing.
At IBI Healthcare Institute we understand the emotional distress that accompanies this type of diagnosis and we are here to help. Treatment for MRKH may include vaginal reconstruction by an expert reconstructive surgeon.
What is MRKH?
Mayer-Rokitansky-Küster-Hauser (MRKH) Syndrome is a rare disorder that affects approximately 1 out of 5000 females each year. The disorder affects the female reproductive system and is tricky to diagnose at first. MRKH disease causes the uterus and/or vagina to be either underdeveloped or not present at all; however, they do still have normal genitalia, ovaries that function properly, and female chromosomes.
All may appear normal including the onset of pubic hair growth and developing breasts as they reach puberty with the disorder normally diagnosed when the menstrual cycle remains absent. Historically this disorder was thought to be a random birth defect but as more research takes place, experts are almost certain that it is genetic and a dominant gene. Either parent that is carrying this dominant gene has a 50% chance of passing it on to their child.
Comparing MRKH Syndrome Reproductive vs Normal Organs
How Do They Diagnose Mayer-Rokitansky-Küster-Hauser Syndrome?
Diagnosis is normally initiated when a teenager fails to begin menstruating.
The doctor will normally begin by performing a physical exam and check for signs of the disorder which include a shortened vagina and then order an ultrasound or MRI imaging tests to determine the advancement of the disorder. In some cases, the kidneys and other organs may be affected as well. Blood tests are also typically ordered to check hormone levels.
Teens diagnosed with MRKH syndrome typically experience identity issues and increased emotional distress at this already sensitive time in their life which leads to depression. Available treatments and emotional therapy should be explored as soon as possible.
If it is discovered that they lack a vaginal canal or the canal is abnormally short and would make normal functionality an issue (such as during sexual intercourse) then Neovagina surgery should be considered. It is a safe and effective procedure that might be an option for them that would restore sexual function.
What Is Neovagina?
Neovagina is a surgical procedure that creates a vaginal canal for patients who suffer from MRKH. Numerous surgical techniques are available to create a neovagina to help those with MRKH
The McIndoe procedure creates a neovagina using a skin graft (generally from the buttocks). This procedure can carry a week of downtime to ensure that the neovagina heals properly.
This involves the creation of a vaginal pouch from the labia minora. The resulting neovagina is too small to engage in sexual intercourse without pain or injury. This procedure has undergone several modifications to form a deeper pouch but is normally only used if other surgical procedures are no longer an option.
This is considered a major operation that involves using a section of the bowel to create the neovagina. The recovery from bowel vagina surgery can extend up to 6 weeks in some cases.
This procedure requires the usage of dilators and a surgical procedure. It involves using a traction device that is placed outside the abdomen. A small bead is placed inside the vagina and the vaginal cavity is formed using continual pressure over the next 7-10 days.
This procedure involves the use of your peritoneal lining (the membrane that lines the abdomen). An incision is made where the vaginal canal is going to be formed. Another incision is then made near the belly button. The peritoneal lining is then stitched to create the vaginal opening and canal. Dilators must be used for a short time after surgery. This surgery is often performed laparoscopically (minimally invasive using small incisions).
Where Can I Get Neovagina Surgery For MRKH in Atlanta?
Neovagina surgery is available at the Advanced Women’s Health Center of IBI Healthcare Institute In Atlanta, GA and requires a surgeon that is highly skilled and extensively trained in plastic and reconstructive vaginal procedures. At IBI Healthcare Institute you will be in the hands of cosmetic surgeons that are experts in vaginoplasty. Choosing IBI Healthcare Institute means choosing the highest standard of care at affordable rates in a state-of-the-art surgical center.
Contact IBI Healthcare Institute to learn more or find out If you are a good candidate for MRKH surgery. Set up your consultation today and speak with one of our highly skilled compassionate professionals.
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